BACKGROUND: Patients with Möbius and Poland-Möbius syndromes may experience paralytic lagophthalmos. METHODS: This is a retrospective interventional case series. We report 1 case of Möbius syndrome and 2 cases of Poland-Möbius syndrome, wherein patients underwent lower blepharoplasty for lagophthalmos with 2 different surgical techniques. RESULTS: Two patients with Poland-Möbius syndrome presenting with bilateral lower eyelid entropion and paralytic lagophthalmos underwent lower eyelid elongation using right auricular cartilage via a transcutaneous approach. One patient with Möbius syndrome presenting with monolateral lower eyelid ectropion and lagophthalmos underwent lower eyelid elongation with Tessier cheek rotation flap. In all cases, lagophthalmos disappeared, and no complications were reported after a mean follow-up period of 19.6 months. CONCLUSIONS: A good functional correction of lagophthalmos was obtained at long-term follow-up with 2 different surgical techniques. In patients with Möbius and Poland-Möbius syndromes, correction of lagophthalmos should be rapidly undertaken to prevent consequences of exposure keratopathy.

Lower eyelid surgery for lagophthalmos in Möbius and Poland-Möbius syndromes.

MAGLI, Adriano;
2011

Abstract

BACKGROUND: Patients with Möbius and Poland-Möbius syndromes may experience paralytic lagophthalmos. METHODS: This is a retrospective interventional case series. We report 1 case of Möbius syndrome and 2 cases of Poland-Möbius syndrome, wherein patients underwent lower blepharoplasty for lagophthalmos with 2 different surgical techniques. RESULTS: Two patients with Poland-Möbius syndrome presenting with bilateral lower eyelid entropion and paralytic lagophthalmos underwent lower eyelid elongation using right auricular cartilage via a transcutaneous approach. One patient with Möbius syndrome presenting with monolateral lower eyelid ectropion and lagophthalmos underwent lower eyelid elongation with Tessier cheek rotation flap. In all cases, lagophthalmos disappeared, and no complications were reported after a mean follow-up period of 19.6 months. CONCLUSIONS: A good functional correction of lagophthalmos was obtained at long-term follow-up with 2 different surgical techniques. In patients with Möbius and Poland-Möbius syndromes, correction of lagophthalmos should be rapidly undertaken to prevent consequences of exposure keratopathy.
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Utilizza questo identificativo per citare o creare un link a questo documento: http://hdl.handle.net/11386/3121450
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